Catecholaminergic polymorphic ventricular tachycardia
Dernière mise à jour 18 Aug 2020
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Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
Description
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
If CPVT is not recognized and treated, an episode of ventricular tachycardia may cause the heart to stop beating (cardiac arrest), leading to sudden death. Researchers suspect that CPVT may be a significant cause of sudden death in children and young adults without recognized heart abnormalities.
Inheritance patterns
The source lists the following possible inheritance patterns: Autosomal dominant; Autosomal recessive. More than one pattern can apply in different cases.
Related genes
Other names
Bidirectional tachycardia induced by catecholamines
Catecholamine-induced polymorphic ventricular tachycardia
CPVT
Familial polymorphic ventricular tachycardia
FPVT
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Lectures complémentaires et références
- Catecholaminergic polymorphic ventricular tachycardia; MedlinePlus, National Library of Medicine.
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